Linear atrophoderma of Moulin located on the face

نویسندگان

  • Selma Emre
  • Ahmet Metin
  • Nuran Sungu
  • Fadime Kilinc
  • Duriye Deniz Demirseren
چکیده

Linear atrophoderma of Moulin (LAM) is a dermatosis characterized by hyperpigmented and depressed band-like lesions localized along the Blaschko lines. This dermatosis was described for the first time by Moulin et al. in five patients with similar characteristics in 1992 and referred to atrophoderma of Moulin, with referrance to the first publication [1,2]. Major characteristics of LAM are being unilateral, following the Blaschko lines, long remain unchanged, onset in the childhood or adolescent period and lack of the induration. The lesions indicate progression over the first few months, then after having a linear atrophic state they stop the progression, limit themselves and become persistent [3]. Despite clinically atrophic appearance of the lesions, elastic and collagen fibers are usually normal in histopathological examination [2]. Etiology of LAM is unknown. Its localization matching the Blaschko lines is thought to be a reflection of mosaicism, which is believed to develop due to a somatic mutation occurring during early embryogenesis [4,5].

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منابع مشابه

Linear atrophoderma of Moulin: a case report and review of the literature

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تاریخ انتشار 2016